NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial
Details
- Name
- NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial
- Synonyms
- CI-13kD-A
- Complex I-13kD-A
- NADH-ubiquinone oxidoreductase 13 kDa-A subunit
- Gene Name
- NDUFS6
- Organism
- Humans
- Amino acid sequence
>lcl|BSEQ0016013|NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial MAAAMTFCRLLNRCGEAARSLPLGARCFGVRVSPTGEKVTHTGQVYDDKDYRRIRFVGRQ KEVNENFAIDLIAEQPVSEVETRVIACDGGGGALGHPKVYINLDKETKTGTCGYCGLQFR QHHH
- Number of residues
- 124
- Molecular Weight
- 13711.535
- Theoretical pI
- 8.38
- GO Classification
- Functionselectron carrier activity / NADH dehydrogenase (ubiquinone) activityProcessescardiovascular system development / cellular metabolic process / fatty acid metabolic process / mitochondrial electron transport, NADH to ubiquinone / mitochondrion morphogenesis / multicellular organism growth / multicellular organismal aging / muscle contraction / reproductive system development / respiratory electron transport chain / small molecule metabolic processComponentsmitochondrial inner membrane / mitochondrial respiratory chain complex I
- General Function
- Nadh dehydrogenase (ubiquinone) activity
- Specific Function
- Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone.
- Pfam Domain Function
- zf-CHCC (PF10276)
- Transmembrane Regions
- Not Available
- Cellular Location
- Mitochondrion inner membrane
- Gene sequence
>lcl|BSEQ0016014|NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial (NDUFS6) ATGGCGGCGGCGATGACCTTCTGCCGGCTGCTGAACCGGTGTGGCGAGGCGGCGCGGAGC CTGCCCCTGGGCGCCAGGTGTTTCGGGGTGCGGGTCTCGCCGACCGGGGAGAAGGTCACG CACACTGGCCAGGTTTATGATGATAAAGACTACAGGAGAATTCGGTTTGTAGGTCGTCAG AAAGAGGTGAATGAAAACTTTGCCATTGATTTGATAGCAGAGCAGCCCGTGAGCGAGGTG GAGACTCGGGTGATAGCGTGCGATGGCGGCGGGGGAGCTCTTGGCCACCCAAAAGTGTAT ATAAACTTGGACAAAGAAACAAAAACCGGCACATGCGGTTACTGTGGGCTCCAGTTCAGA CAGCACCACCACTAG
- Chromosome Location
- 5
- Locus
- 5p15.33
- External Identifiers
Resource Link UniProtKB ID O75380 UniProtKB Entry Name NDUS6_HUMAN GenBank Protein ID 3348137 GenBank Gene ID AF044959 GenAtlas ID NDUFS6 HGNC ID HGNC:7713 - General References
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