Search
Cardiolipin Biosynthesis CL(13:0/a-13:0/i-13:0/i-13:0)
smpdb.ca/view/SMP0196288MetabolicSixth, phosphatidylglycerophosphatase and protein-tyrosine phosphatase dephosphorylates PGP to form phosphatidylglycerol (PG). … Cardiolipin (CL) is an important component of the inner mitochondrial membrane where it constitutes about 20% of the total lipid composition.
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(13:0/a-13:0/a-13:0/a-13:0)
smpdb.ca/view/SMP0196202MetabolicSixth, phosphatidylglycerophosphatase and protein-tyrosine phosphatase dephosphorylates PGP to form phosphatidylglycerol (PG). … Cardiolipin (CL) is an important component of the inner mitochondrial membrane where it constitutes about 20% of the total lipid composition.
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/a-13:0/a-13:0)
smpdb.ca/view/SMP0043663DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/a-13:0/i-13:0)
smpdb.ca/view/SMP0043669DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/i-13:0/a-13:0)
smpdb.ca/view/SMP0043770DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/i-13:0/a-13:0/i-13:0)
smpdb.ca/view/SMP0045604DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/i-13:0/i-13:0/i-13:0)
smpdb.ca/view/SMP0045709DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/a-13:0/a-13:0/a-13:0)
smpdb.ca/view/SMP0055281DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/a-13:0/i-13:0/i-13:0)
smpdb.ca/view/SMP0055396DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/a-13:0/a-13:0/i-13:0)
smpdb.ca/view/SMP0055287DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1