Search
Cardiolipin Biosynthesis CL(i-13:0/a-13:0/i-13:0/a-13:0)
smpdb.ca/view/SMP0055390DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/i-13:0/i-13:0/a-13:0)
smpdb.ca/view/SMP0057333DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/i-13:0/i-13:0/i-13:0)
smpdb.ca/view/SMP0057339DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/i-13:0/i-13:0)
smpdb.ca/view/SMP0043776DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/i-13:0/a-13:0/a-13:0)
smpdb.ca/view/SMP0045598DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/i-13:0/i-13:0/a-13:0)
smpdb.ca/view/SMP0045703DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/i-13:0/a-13:0/a-13:0)
smpdb.ca/view/SMP0057225DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(i-13:0/i-13:0/a-13:0/i-13:0)
smpdb.ca/view/SMP0057231DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164). … BTHS patients seem to lack acyl specificity and consequently, many potential cardiolipin species can exist (PMID: 16226238).
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/a-13:0/a-13:0)[rac]
smpdb.ca/view/SMP0356177MetabolicSixth, phosphatidylglycerophosphatase and protein-tyrosine phosphatase dephosphorylates PGP to form phosphatidylglycerol (PG). … Cardiolipin (CL) is an important component of the inner mitochondrial membrane where it constitutes about 20% of the total lipid composition.
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1Cardiolipin Biosynthesis CL(a-13:0/a-13:0/a-13:0/i-13:0)[rac]
smpdb.ca/view/SMP0356183MetabolicSixth, phosphatidylglycerophosphatase and protein-tyrosine phosphatase dephosphorylates PGP to form phosphatidylglycerol (PG). … Cardiolipin (CL) is an important component of the inner mitochondrial membrane where it constitutes about 20% of the total lipid composition.
Drugs: NADH · Cytidine-5'-Triphosphate · sn-glycerol 3-phosphate · Pyrophosphoric acid · Dihydroxyacetone phosphateEnzymes: Phosphatidylglycerophosphatase and protein-tyrosine phosphatase 1