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Cardiolipin Biosynthesis CL(i-13:0/a-25:0/i-21:0/a-25:0)
smpdb.ca/view/SMP0056836DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/a-25:0/i-22:0/a-25:0)
smpdb.ca/view/SMP0056854DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/a-25:0/i-24:0/a-25:0)
smpdb.ca/view/SMP0056872DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/i-12:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0056979DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/i-13:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0057301DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/i-17:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0058601DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-13:0/i-21:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0059936DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-14:0/i-12:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0061742DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(i-14:0/i-15:0/a-25:0/a-25:0)
smpdb.ca/view/SMP0062714DiseaseA mutated tafazzin gene disrupts this post-synthetic remodeling and causes Barth syndrome (BTHS), an X-linked human disease (PMID: 16973164).
Cardiolipin Biosynthesis CL(10:0/18:2(9Z,11Z)/a-25:0/a-25:0)
smpdb.ca/view/SMP0178822MetabolicCardiolipin (CL) is an important component of the inner mitochondrial membrane where it constitutes about 20% of the total lipid composition. It is essential for the optimal function of numerous enzymes that are involved in mitochondrial...