| Acylcarnitine (2R,3R)-3-Hydroxy-2-methylbutanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2R,3R,4E)-2,3-dihydroxy-5-(methylsulfanyl)pent-4-enoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2R,3S)-3-Hydroxy-2-methylbutanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S)-2-hydroxy-2-(propan-2-yl)butanedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S)-2-hydroxydecanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S)-2-hydroxyhexadecanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S)-2-hydroxyoctadecanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S,3R)-3-Hydroxy-2-methylbutanoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2S,3R)-3-hydroxy-2-methylpentanedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-2-(propan-2-yl)but-2-enedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-5-Hydroxydec-2-enedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-5-Hydroxydec-2-enoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-6-hydroxynon-2-enoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-dec-2-enedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-non-2-enoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z)-oct-2-enedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,4E)-Deca-2,4-dienedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,4E,6Z)-Decatrienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,4Z)-octa-2,4-dienedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,5E,7E)-Deca-2,5,7-trienedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,5Z,9Z)-hexadeca-2,5,9-trienedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (2Z,6Z,10Z)-hexadeca-2,6,10-trienedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (3,5)-Decadienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine (3,6)-Decadienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |