Search

Displaying results 6621 - 6630 of 10000 in total
  1. Pathway

    Acylcarnitine 2-Hydroxydodeca-4,6-dienoylcarnitine

    smpdb.ca/view/SMP0124046
    Metabolic

    2-Hydroxydodeca-4,6-dienoylcarnitine is an acylcarnitine. … Once in the matrix, 2-hydroxydodeca-4,6-dienoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 2-hydroxydodeca-4,6-dienoyl-CoA

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  2. Pathway

    Acylcarnitine 2-Hydroxytrtradeca-4,6-dienoylcarnitine

    smpdb.ca/view/SMP0124182
    Metabolic

    2-Hydroxytrtradeca-4,6-dienoylcarnitine is an acylcarnitine. … Once in the matrix, 2-hydroxytrtradeca-4,6-dienoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 2-hydroxytrtradeca-

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  3. Pathway

    Acylcarnitine (2E)-Pentadec-2-enoylcarnitine

    smpdb.ca/view/SMP0124230
    Metabolic

    (2E)-Pentadec-2-enoylcarnitine is an acylcarnitine. … Once in the matrix, (2E)-pentadec-2-enoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form (2E)-pentadec-2-enoyl-CoA and

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  4. Pathway

    2-Ketoglutarate Dehydrogenase Complex Deficiency

    smpdb.ca/view/SMP0125755
    Disease

    OGDC catalyzes the conversion of 2-ketoglutarate into succinyl-CoA. This disorder is characterized by a large accumulation of 2-ketoglutarate in the urine. … 2-Ketoglutarate dehydrogenase complex deficiency, also known as alpha-ketoglutarate dehydrogenase deficiency or oxoglutaric aciduria, is an autosomal recessive disorder of the Krebs cycle caused by a defective

    Drugs: Pyruvic acid · Biotin · Succinic acid · NADH · ATP · Magnesium cation +4 more
    Enzymes: 2-oxoglutarate dehydrogenase, mitochondrial, Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial
  5. Pathway

    Acylcarnitine (2E)-hept-2-enedioylcarnitine

    smpdb.ca/view/SMP0123359
    Metabolic

    (2E)-hept-2-enedioylcarnitine is an acylcarnitine. … Once in the matrix, (2E)-hept-2-enedioylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form (2E)-hept-2-enedioyl-CoA and

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  6. Pathway

    Acylcarnitine 2-hydroxyoct-4-enedioylcarnitine

    smpdb.ca/view/SMP0123385
    Metabolic

    2-hydroxyoct-4-enedioylcarnitine is an acylcarnitine. … Once in the matrix, 2-hydroxyoct-4-enedioylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 2-hydroxyoct-4-enedioyl-CoA

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  7. Pathway

    Acylcarnitine (2Z)-non-2-enoylcarnitine

    smpdb.ca/view/SMP0123414
    Metabolic

    (2Z)-non-2-enoylcarnitine is an acylcarnitine. … Once in the matrix, (2Z)-non-2-enoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form (2Z)-non-2-enoyl-CoA and L-carnitine

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  8. Pathway

    Acylcarnitine (2E)-non-2-enedioylcarnitine

    smpdb.ca/view/SMP0123428
    Metabolic

    (2E)-non-2-enedioylcarnitine is an acylcarnitine. … Once in the matrix, (2E)-non-2-enedioylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form (2E)-non-2-enedioyl-CoA and L-carnitine

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  9. Pathway

    Acylcarnitine 4-(methylsulfanyl)-2-oxobutanoylcarnitine

    smpdb.ca/view/SMP0123536
    Metabolic

    4-(methylsulfanyl)-2-oxobutanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 4-(methylsulfanyl)-2-oxobutanoyl-CoA reacts with L-carnitine to form 4-(methylsulfanyl)-2-oxobutanoylcarnitine.

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial
  10. Pathway

    Acylcarnitine 5-hydroxy-2-propylpentanoylcarnitine

    smpdb.ca/view/SMP0123563
    Metabolic

    5-hydroxy-2-propylpentanoylcarnitine is an acylcarnitine. … Once in the matrix, 5-hydroxy-2-propylpentanoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 5-hydroxy-2-propylpentanoyl-CoA

    Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 more
    Enzymes: Carnitine O-palmitoyltransferase 2, mitochondrial