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Acylcarnitine 5-Hydroxydec-5-enoylcarnitine
smpdb.ca/view/SMP0123869Metabolic5-Hydroxydec-5-enoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxydec-5-enoyl-CoA reacts with L-carnitine to form 5-hydroxydec-5-enoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Hydroxydec-5-enedioylcarnitine
smpdb.ca/view/SMP0123883Metabolic5-Hydroxydec-5-enedioylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxydec-5-enedioyl-CoA reacts with L-carnitine to form 5-hydroxydec-5-enedioylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-(3,4-dimethyl-5-pentylfuran-2-yl)pentanoylcarnitine
smpdb.ca/view/SMP0123510Metabolic5-(3,4-dimethyl-5-pentylfuran-2-yl)pentanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-(3,4-dimethyl-5-pentylfuran-2-yl)pentanoyl-CoA reacts with L-carnitine to form 5-(3,4-dimethyl-5-pentylfuran-2-yl)pentanoylcarnitine.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-(3-methyl-5-pentylfuran-2-yl)pentanoylcarnitine
smpdb.ca/view/SMP0123511Metabolic5-(3-methyl-5-pentylfuran-2-yl)pentanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-(3-methyl-5-pentylfuran-2-yl)pentanoyl-CoA reacts with L-carnitine to form 5-(3-methyl-5-pentylfuran-2-yl)pentanoylcarnitine.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 55-Oxoprolinuria
smpdb.ca/view/SMP0125615Disease5-Oxoprolinuria (5-Oxoprolinase deficiency) is a result of a defect in the gamma-glutamyl cycle due to either 5-oxoprolinase or glutathione synthetase deficiency. … In the case of 5-oxoprolinase, however, pyroglutamic acid accumulates. Symptoms include anemia, mental retardation, metabolic acidosis, respiratory distress and urolithiasis.
Enzymes: 5-oxoprolinaseAcylcarnitine 5-(5-heptyl-3-methylfuran-2-yl)pentanoylcarnitine
smpdb.ca/view/SMP0123512Metabolic5-(5-heptyl-3-methylfuran-2-yl)pentanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-(5-heptyl-3-methylfuran-2-yl)pentanoyl-CoA reacts with L-carnitine to form 5-(5-heptyl-3-methylfuran-2-yl)pentanoylcarnitine.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 55-Oxoprolinuria
smpdb.ca/view/SMP0000143Disease5-Oxoprolinuria (5-Oxoprolinase deficiency) is a result of a defect in the gamma-glutamyl cycle due to either 5-oxoprolinase or glutathione synthetase deficiency. … In the case of 5-oxoprolinase, however, pyroglutamic acid accumulates. Symptoms include anemia, mental retardation, metabolic acidosis, respiratory distress and urolithiasis.
Enzymes: 5-oxoprolinase5-Oxoprolinase Deficiency
smpdb.ca/view/SMP0000500Disease5-Oxoprolinase deficiency, also called OPLAHD, is a rare inborn error of metabolism (IEM) and autosomal recessive disorder of glutathione metabolism caused by a defective 5-oxoprolinase. 5-Oxoprolinase … This disorder is characterized by a large accumulation of 5-oxoproline in the urine.
Enzymes: 5-oxoprolinaseAcylcarnitine 5-octenoylcarnitine
smpdb.ca/view/SMP0123372Metabolic5-octenoylcarnitine is an acylcarnitine. … Once in the matrix, 5-octenoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 5-octenoyl-CoA and L-carnitine. 5-octenoyl-CoA
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Methylnonanoylcarnitine
smpdb.ca/view/SMP0123580Metabolic5-Methylnonanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-methylnonanoyl-CoA reacts with L-carnitine to form 5-methylnonanoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5