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Acylcarnitine 3-methyloctanedioylcarnitine
smpdb.ca/view/SMP0123847MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … As part of this process, 3-methyloctanedioic acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1).
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-oxodecanoylcarnitine
smpdb.ca/view/SMP0123927MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … As part of this process, 3-oxodecanoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1).
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-Hydroxydodecanedioylcarnitine
smpdb.ca/view/SMP0124079MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … and L-carnitine. 3-Hydroxydodecanedioyl-CoA then enters into the mitochondrial beta-oxidation pathway to form aceytl-CoA.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-oxododecanoylcarnitine
smpdb.ca/view/SMP0124082MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … As part of this process, 3-oxododecanoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1).
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-hydroxytridecanoylcarnitine
smpdb.ca/view/SMP0124099MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … As part of this process, 3-hydroxytridecanoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1).
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-oxohexadecanoylcarnitine
smpdb.ca/view/SMP0124303MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … As part of this process, 3-oxohexadecanoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1).
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 1Acylcarnitine 3-hydroxyheptadecanoylcarnitine
smpdb.ca/view/SMP0124304MetabolicThe general role of acylcarnitines is to transport acyl-groups, organic acids and fatty acids, from the cytoplasm into the mitochondria so that they can be broken down to produce energy. … and L-carnitine. 3-hydroxyheptadecanoyl-CoA then enters into the mitochondrial beta-oxidation pathway to form aceytl-CoA.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Long-chain-fatty-acid--CoA ligase 1, Long-chain fatty acid transport protein 13-Hydroxyisobutyric Aciduria
smpdb.ca/view/SMP0125674DiseaseSigns and symptoms of 3-hydroxyisobutyric aciduria include developmental delay, dysmorphic facial features, and brain abnormalities. … The excretion of 3-hydroxyisobutyric acid in the urine can range from 170 to 390 mmol/mol of creatinine.
Enzymes: 3-ketoacyl-CoA thiolase, mitochondrial, 3-hydroxyacyl-CoA dehydrogenase type-2De Novo Triacylglycerol Biosynthesis TG(20:3(5Z,8Z,11Z)/20:3(5Z,8Z,11Z)/18:3(6Z,9Z,12Z))
smpdb.ca/view/SMP0023178MetabolicA triglyceride (TG, triacylglycerol, TAG, or triacylglyceride) is an ester derived from glycerol and three fatty acids. … Last, the enzyme diacylglycerol O-acyltransferase synthesizes triacylglycerol from diacylglycerol and a fatty acyl-CoA.
Enzymes: 1-Acyl-sn-glycerol-3-phosphate acyltransferase alpha, Glycerol-3-phosphate dehydrogenase [NAD(+)], cytoplasmicDe Novo Triacylglycerol Biosynthesis TG(20:3(5Z,8Z,11Z)/20:3(5Z,8Z,11Z)/18:3(9Z,12Z,15Z))
smpdb.ca/view/SMP0023183MetabolicA triglyceride (TG, triacylglycerol, TAG, or triacylglyceride) is an ester derived from glycerol and three fatty acids. … Last, the enzyme diacylglycerol O-acyltransferase synthesizes triacylglycerol from diacylglycerol and a fatty acyl-CoA.
Enzymes: 1-Acyl-sn-glycerol-3-phosphate acyltransferase alpha, Glycerol-3-phosphate dehydrogenase [NAD(+)], cytoplasmic