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Acylcarnitine 5-Methyloctanoylcarnitine
smpdb.ca/view/SMP0123843Metabolic5-Methyloctanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-methyloctanoyl-CoA reacts with L-carnitine to form 5-methyloctanoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Hydroxydecanoylcarnitine
smpdb.ca/view/SMP0123854Metabolic5-Hydroxydecanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxydecanoyl-CoA reacts with L-carnitine to form 5-hydroxydecanoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Decenoylcarnitine
smpdb.ca/view/SMP0123863Metabolic5-Decenoylcarnitine is an acylcarnitine. … Once in the matrix, 5-decenoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 5-decenoyl-CoA and L-carnitine. 5-Decenoyl-CoA
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Hydroxydecanedioylcarnitine
smpdb.ca/view/SMP0123925Metabolic5-Hydroxydecanedioylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxydecanedioyl-CoA reacts with L-carnitine to form 5-hydroxydecanedioylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Oxodecanoylcarnitine
smpdb.ca/view/SMP0123930Metabolic5-Oxodecanoylcarnitine is an acylcarnitine. … Once in the matrix, 5-oxodecanoylcarnitine can react with the carnitine O-palmitoyltransferase 2 enzyme found in the mitochondrial inner membrane to once again form 5-oxodecanoyl-CoA and L-carnitine. 5
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-Hydroxyundecanoylcarnitine
smpdb.ca/view/SMP0123940Metabolic5-Hydroxyundecanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxyundecanoyl-CoA reacts with L-carnitine to form 5-hydroxyundecanoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-hydroxyhexadecanoylcarnitine
smpdb.ca/view/SMP0124252Metabolic5-hydroxyhexadecanoylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxyhexadecanoyl-CoA reacts with L-carnitine to form 5-hydroxyhexadecanoylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 5Acylcarnitine 5-hydroxyhexadecanedioylcarnitine
smpdb.ca/view/SMP0124302Metabolic5-hydroxyhexadecanedioylcarnitine is an acylcarnitine. … In forming an acylcarnitine derivative, 5-hydroxyhexadecanedioyl-CoA reacts with L-carnitine to form 5-hydroxyhexadecanedioylcarnitine. This reaction is catalyzed by carnitine O-palmitoyltransferase.
Drugs: Biotin · Adenosine phosphate · ATP · Levocarnitine · Magnesium cation · Pyrophosphoric acid +1 moreEnzymes: Solute carrier family 22 member 55-Oxoprolinase Deficiency
smpdb.ca/view/SMP0125617Disease5-Oxoprolinase deficiency, also called OPLAHD, is a rare inborn error of metabolism (IEM) and autosomal recessive disorder of glutathione metabolism caused by a defective 5-oxoprolinase. 5-Oxoprolinase … This disorder is characterized by a large accumulation of 5-oxoproline in the urine.
Enzymes: 5-oxoprolinasePhosphatidylethanolamine Biosynthesis PE(20:5(6E,8Z,11Z,14Z,17Z)-OH(5)/15:0)
smpdb.ca/view/SMP0127519MetabolicPhosphatidylethanolamines (PE) are a class of phospholipids that incorporate a phosphoric acid headgroup into a diacylglycerol backbone. They are the second most abundant phospholipid in eukaryotic cell membranes, and contrary to phospha...