| Acylcarnitine Undeca-4,7-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-4,8-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-4,9-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-5,7-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-5,8-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-5,9-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-6,8-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-6,9-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undeca-7,9-dienoylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Acylcarnitine Undecanedioylcarnitine |  | Metabolic | Biotin / Adenosine phosphate / ATP / Levocarnitine / Magnesium cation / Pyrophosphoric acid / Malonyl-CoA |
| Adefovir Dipivoxil Action Pathway |  | Drug Action | ATP |
| Adefovir Dipivoxil Action Pathway (New) |  | Drug Action | Adefovir dipivoxil / Magnesium cation |
| Adefovir Dipivoxil Metabolism Pathway |  | Drug Metabolism | ATP / Adefovir dipivoxil / Magnesium cation |
| Adenine Phosphoribosyltransferase Deficiency (APRT) |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenine Phosphoribosyltransferase Deficiency (APRT) |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenosine Deaminase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenosine Deaminase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenylosuccinate Lyase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenylosuccinate Lyase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Uric acid / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenoleukodystrophy, X-Linked |  | Disease | ATP / Levocarnitine / Magnesium cation / Lauric acid |
| Adrenoleukodystrophy, X-Linked |  | Disease | ATP / Levocarnitine / Magnesium cation / Lauric acid |