Complement Inactivating Agents

Name
Complement Inactivating Agents
Accession Number
DBCAT001769
Description

Compounds that negatively regulate the cascade process of COMPLEMENT ACTIVATION. Uncontrolled complement activation and resulting cell lysis is potentially dangerous for the host.

ATC Classification
Drugs
DrugDrug Description
EculizumabA recombinant humanized monoclonal antibody used to reduce the risk of hemolysis in paroxysmal nocturnal hemoglobinuria (PNH) and atypical hemolytic uremic syndrome (aHUS).
IcatibantA bradykinin B2 receptor antagonist used to treat acute episodes of swelling and inflammation associated with hereditary angioedema (HAE).
Human C1-esterase inhibitorA C1 inhibitor used to prevent angioedema attacks associated with hereditary angioedema.
NafamostatUsed as an anticoagulant in patients with disseminative blood vessel coagulation, hemorrhagic lesions, and hemorrhagic tendencies. It prevents blood clot formation during extracorporeal circulation in patients undergoing continuous renal replacement...
RavulizumabA monoclonal antibody used to treat paroxysmal nocturnal hemoglobinuria, atypical hemolytic uremic syndrome, and myasthenia gravis.
PegcetacoplanA complement inhibitor indicated in the treatment of adults with paroxysmal nocturnal hemoglobinuria.
VilobelimabAn antibody directed against anti-human complement factor 5a is used to treat COVID-19 in adults for emergency use.
FasitibantFasitibant is under investigation in clinical trial NCT02205814 (Fasitibant Intra-articular Injection in Patients With Symptomatic Osteoarthritis of the Knee).
Avacincaptad pegolAn RNA aptamer inhibiting the complement C5 indicated for the treatment of geographic atrophy secondary to age-related macular degeneration.
PozelimabA human monoclonal IgG4 antibody used to treat CD55-deficient protein-losing enteropathy (PLE) or CHAPLE disease
ZilucoplanA complement inhibitor used to treat generalized myasthenia gravis in anti-acetylcholine receptor (AChR) antibody-positive adults.
DanicopanA small molecule complement factor D inhibitor used to treat extravascular hemolysis in patients with paroxysmal nocturnal hemoglobinuria.
SutimlimabA monoclonal antibody directed towards complement subunit C1s used to reduce the need for blood transfusion due to hemolysis in patients with cold agglutinin disease.
AvacopanAn orally bioavailable complement 5a receptor (C5aR) antagonist for the treatment of severe anti-neutrophil cytoplasmic (auto)antibody (ANCA)-associated vasculitis.
CrovalimabA complement C5 inhibiting antibody used to treat paroxysmal nocturnal hemoglobinuria in adults and adolescents.
IptacopanA factor B inhibitor used to treat paroxysmal nocturnal hemoglobinuria.
Drugs & Drug Targets
DrugTargetType
EculizumabComplement C5target
IcatibantB2 bradykinin receptortarget
IcatibantAminopeptidase Ntarget
Human C1-esterase inhibitorComplement C1r subcomponenttarget
Human C1-esterase inhibitorComplement C1s subcomponenttarget
Human C1-esterase inhibitorPlasma kallikreintarget
Human C1-esterase inhibitorCoagulation factor XIItarget
Human C1-esterase inhibitorProthrombintarget
Human C1-esterase inhibitorCoagulation factor XItarget
Human C1-esterase inhibitorTissue-type plasminogen activatortarget
NafamostatIntercellular adhesion molecule 1target
NafamostatSerine protease 1target
NafamostatKallikrein-1target
NafamostatProthrombintarget
NafamostatCoagulation factor Xtarget
NafamostatCoagulation factor XIItarget
NafamostatSolute carrier family 22 member 1transporter
NafamostatSolute carrier family 22 member 2transporter
NafamostatTumor necrosis factortarget
RavulizumabComplement C5target
PegcetacoplanComplement C3target
VilobelimabComplement C5target
FasitibantB2 bradykinin receptortarget
Avacincaptad pegolComplement C5target
PozelimabComplement C5target
ZilucoplanComplement C5target
ZilucoplanCytochrome P450 4F2enzyme
DanicopanBroad substrate specificity ATP-binding cassette transporter ABCG2transporter
DanicopanATP-dependent translocase ABCB1transporter
DanicopanComplement factor Dtarget
SutimlimabComplement C1s subcomponenttarget
AvacopanC5a anaphylatoxin chemotactic receptor 1target
AvacopanCytochrome P450 3A4enzyme
AvacopanATP-dependent translocase ABCB1transporter
AvacopanCytochrome P450 1A2enzyme
AvacopanCytochrome P450 2B6enzyme
AvacopanCytochrome P450 2C9enzyme
CrovalimabComplement C5target
IptacopanCytochrome P450 2C8enzyme
IptacopanCytochrome P450 2D6enzyme
IptacopanUDP-glucuronosyltransferase 1A1enzyme
IptacopanUDP-glucuronosyltransferase 1A3enzyme
IptacopanUDP-glucuronosyltransferase 1A8enzyme
IptacopanComplement factor Btarget
IptacopanAlbumincarrier
IptacopanAlpha-1-acid glycoprotein 1carrier