| Glutaric Aciduria Type I |  | Disease | Pyridoxal phosphate / Lysine / Glutamic acid / NADH / Oxogluric acid / Flavin adenine dinucleotide / L-Saccharopine |
| Glutaric Aciduria Type I |  | Disease | Adenosine phosphate / NADH / ATP / Levocarnitine / Magnesium cation / Flavin adenine dinucleotide / Palmitic Acid / Pyrophosphoric acid |
| Glutaric Aciduria Type I (Fatty Acid Metabolism) |  | Disease | Adenosine phosphate / NADH / ATP / Levocarnitine / Magnesium cation / Flavin adenine dinucleotide / Glutaric Acid / Palmitic Acid / Pyrophosphoric acid / 3-hydroxyglutaric acid |
| Glutaric Aciduria Type I (Lysine Degradation) |  | Disease | Pyridoxal phosphate / Lysine / Glutamic acid / NADH / Oxogluric acid / Flavin adenine dinucleotide / L-Saccharopine / 3-hydroxyglutaric acid |
| Glutathione Metabolism |  | Metabolic | Glutamic acid / Glutathione / Glycine / Cysteine / Alanine / ATP / Zinc / Pidolic acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / S-Methyl glutathione |
| Glutathione Synthetase Deficiency |  | Disease | Glutamic acid / Glutathione / Glycine / Cysteine / Alanine / ATP / Zinc / Pidolic acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / S-Methyl glutathione |
| Glutathione Synthetase Deficiency |  | Disease | Glutamic acid / Glutathione / Glycine / Cysteine / Alanine / ATP / Zinc / Pidolic acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / S-Methyl glutathione |
| Glutethimide Action Pathway |  | Drug Action | Pyridoxal phosphate / Glutamic acid / ATP / Morphine / Codeine / Calcium / Magnesium cation / Glutethimide / Cyclic adenosine monophosphate / gamma-Aminobutyric acid / Mesoheme / Pyrophosphoric acid |
| Glutethimide Drug Metabolism |  | Metabolic | Glutethimide |
| Glyburide Action Pathway |  | Drug Action | ATP / Glyburide / Potassium cation / Calcium |
| Glycerin Drug Metabolism |  | Metabolic | Glycerin |
| Glycerol Kinase Deficiency |  | Disease | NADH / ATP / sn-glycerol 3-phosphate / Flavin adenine dinucleotide / Palmitic Acid / Glycerin / Dihydroxyacetone phosphate |
| Glycerol Kinase Deficiency |  | Disease | NADH / ATP / sn-glycerol 3-phosphate / Flavin adenine dinucleotide / Palmitic Acid / Glycerin / Dihydroxyacetone phosphate |
| Glycerol Phosphate Shuttle |  | Metabolic | NADH / D-glyceraldehyde 3-phosphate / sn-glycerol 3-phosphate / Flavin adenine dinucleotide / Dihydroxyacetone phosphate |
| Glycerolipid Metabolism |  | Metabolic | NADH / ATP / sn-glycerol 3-phosphate / Flavin adenine dinucleotide / Palmitic Acid / Glycerin / Dihydroxyacetone phosphate |
| Glycine and Serine Metabolism |  | Metabolic | Pyridoxal phosphate / Tetrahydrofolic acid / Ademetionine / Pyruvic acid / Arginine / Adenosine phosphate / Serine / Methionine / Glutamic acid / Glycine / Creatine / Cysteine / NADH / Alanine / ATP / Aminolevulinic acid / Magnesium cation / Zinc / N,N-dimethylglycine / Glycocyamine / Oxogluric acid / 3-Hydroxypyruvic Acid / Orotidylic acid / Flavin adenine dinucleotide / Pyruvaldehyde / Formaldehyde / 2-Amino-3-Ketobutyric Acid / D-Serine / Pyrophosphoric acid / Glyoxylic acid / Dexfosfoserine / 2-Oxobutanoic Acid |
| Glycine N-Methyltransferase Deficiency |  | Disease | Pyridoxal phosphate / Tetrahydrofolic acid / Ademetionine / Choline / Adenosine phosphate / Serine / Methionine / Glycine / Cysteine / NADH / ATP / Adenosine / Potassium cation / Magnesium cation / Zinc / Putrescine / N,N-dimethylglycine / 4-methylthio-2-oxobutanoic acid / Flavin adenine dinucleotide / Spermidine / Pyrophosphoric acid / L-Homoserine / 2-Oxobutanoic Acid |
| Glycine N-Methyltransferase Deficiency |  | Disease | Pyridoxal phosphate / Tetrahydrofolic acid / Ademetionine / Choline / Adenosine phosphate / Serine / Methionine / Glycine / Cysteine / NADH / ATP / Adenosine / Potassium cation / Magnesium cation / Zinc / Putrescine / N,N-dimethylglycine / 4-methylthio-2-oxobutanoic acid / Flavin adenine dinucleotide / Spermidine / Pyrophosphoric acid / L-Homoserine / 2-Oxobutanoic Acid |
| Glycogen Storage Disease Type 1A (GSD1A) or Von Gierke Disease |  | Disease | Pyruvic acid / Biotin / NADH / ATP / Magnesium cation / 2-phospho-D-glyceric acid / Phosphoenolpyruvate / D-glyceraldehyde 3-phosphate / Oxogluric acid / Dihydroxyacetone phosphate |
| Glycogen Storage Disease Type 1A (GSD1A) or Von Gierke Disease |  | Disease | Pyruvic acid / Biotin / NADH / ATP / Magnesium cation / 2-phospho-D-glyceric acid / Phosphoenolpyruvate / D-glyceraldehyde 3-phosphate / Oxogluric acid / Dihydroxyacetone phosphate |
| Glycogen Synthetase Deficiency |  | Disease | Pyridoxal phosphate / NADH / ATP / Calcium / Magnesium cation / Uridine diphosphate glucose / Maltose / Uridine-5'-Diphosphate / Pyrophosphoric acid / Fructose |
| Glycogen Synthetase Deficiency |  | Disease | Pyridoxal phosphate / NADH / ATP / Calcium / Magnesium cation / Uridine diphosphate glucose / Maltose / Uridine-5'-Diphosphate / Pyrophosphoric acid / Fructose |
| Glycogenosis, Type IA. Von Gierke Disease |  | Disease | Pyruvic acid / Biotin / NADH / ATP / Magnesium cation / 2-phospho-D-glyceric acid / Phosphoenolpyruvate / D-glyceraldehyde 3-phosphate / Oxogluric acid / Dihydroxyacetone phosphate |
| Glycogenosis, Type IA. Von Gierke Disease |  | Disease | Pyruvic acid / Biotin / NADH / ATP / Magnesium cation / 2-phospho-D-glyceric acid / Phosphoenolpyruvate / D-glyceraldehyde 3-phosphate / Oxogluric acid / Dihydroxyacetone phosphate |
| Glycogenosis, Type IB |  | Disease | Pyruvic acid / Biotin / NADH / ATP / Magnesium cation / 2-phospho-D-glyceric acid / Phosphoenolpyruvate / D-glyceraldehyde 3-phosphate / Oxogluric acid / Dihydroxyacetone phosphate |