| Acenocoumarol Action Pathway |  | Drug action | Phylloquinone / Calcium / Acenocoumarol |
| Acetaminophen Action Pathway |  | Drug action | Glutamic acid / Glutathione / Acetaminophen / Dinoprostone / Calcium / Magnesium cation / Zinc / Prostaglandin D2 / Mesoheme / Prostaglandin G2 / Arachidonic Acid |
| Acetaminophen Metabolism Pathway |  | Drug metabolism | Glutathione / NADH / ATP / Acetaminophen / Mesoheme / Uridine-5'-Diphosphate |
| Acetylsalicylic Acid Action Pathway |  | Drug action | Glutamic acid / Glutathione / Dinoprostone / Acetylsalicylic acid / Calcium / Magnesium cation / Zinc / Prostaglandin D2 / Mesoheme / Prostaglandin G2 / Arachidonic Acid |
| Acrivastine H1-Antihistamine Action |  | Drug action | Calcium / Acrivastine |
| Activation of PKC Through G Protein-Coupled Receptor |  | Signaling | Calcium |
| Acute Intermittent Porphyria |  | Disease | Pyridoxal phosphate / Glycine / NADH / Aminolevulinic acid / Iron / Zinc / Protoporphyrin / Mesoheme / Flavin adenine dinucleotide / Uridine-5'-Diphosphate / Coproporphyrinogen III / Farnesyl diphosphate |
| Adefovir Dipivoxil Action Pathway |  | Drug action | ATP |
| Adefovir Dipivoxil Metabolism Pathway |  | Drug metabolism | ATP / Adefovir dipivoxil / Magnesium cation |
| Adenine Phosphoribosyltransferase Deficiency (APRT) |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenosine Deaminase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adenylosuccinate Lyase Deficiency |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia Due to 21-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia Due to 17 alpha-Hydroxylase Deficiency |  | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
| Adrenoleukodystrophy, X-Linked |  | Disease | ATP / Levocarnitine / Magnesium cation / Lauric acid |
| AICA-Ribosiduria |  | Disease | Tetrahydrofolic acid / Aspartic acid / L-Glutamine / Adenosine phosphate / Glutamic acid / Glycine / NADH / ATP / Adenine / Adenosine / Potassium cation / Calcium / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / AICA ribonucleotide / Guanosine-5'-Monophosphate / Xanthine / Guanine / Cyclic adenosine monophosphate / Mesoheme / Guanosine / Ribose-1-Phosphate / Flavin adenine dinucleotide / Hypoxanthine / Pyrophosphoric acid / Maleic acid / Inosine / 2'-Deoxyguanosine-5'-Monophosphate |
| Alanine Metabolism |  | Metabolic | Pyridoxal phosphate / Pyruvic acid / Biotin / Adenosine phosphate / Glutamic acid / Glycine / Alanine / ATP / Zinc / Pyrophosphoric acid / Glyoxylic acid |
| Alcaftadine H1-Antihistamine Action |  | Drug action | Calcium / Alcaftadine |
| Alendronate Action Pathway |  | Drug action | Cholecalciferol / ATP / Alendronic acid / Magnesium cation / Iron / Dimethylallyl Diphosphate / Formic acid / Geranyl Diphosphate / Mesoheme / Flavin adenine dinucleotide / Palmitic Acid / Pyrophosphoric acid / Cholesterol / ISOPENTENYL PYROPHOSPHATE / Farnesyl diphosphate |
| Alfentanil Action Pathway |  | Drug action | ATP / Norepinephrine / Alfentanil / Dopamine / Potassium cation / Calcium |
| Alimemazine H1-Antihistamine Action |  | Drug action | Alimemazine / Calcium |
| Alkaptonuria |  | Disease | Pyridoxal phosphate / Ademetionine / Ascorbic acid / Aspartic acid / Tyrosine / Glutamic acid / NADH / Sapropterin / Norepinephrine / Epinephrine / Dopamine / Levodopa / Calcium / Magnesium cation / Iron / Zinc / 2-(3,4-Dihydroxyphenyl)Acetic Acid / Acetoacetic acid / Methylamine / 1,2-Dihydroxybenzene / Flavin adenine dinucleotide / Pyrroloquinoline Quinone / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Alpha Linolenic Acid and Linoleic Acid Metabolism |  | Metabolic | alpha-Linolenic acid / Dihomo-gamma-linolenic acid / Icosapent / Calcium / Arachidonic Acid |
| Alprenolol Action Pathway |  | Drug action | ATP / Alprenolol / Potassium cation / Calcium / Magnesium cation |
| Alteplase Action Pathway |  | Drug action | Alteplase / Phylloquinone / Calcium |