| Tyrosinemia Type 3 (TYRO3) |  | Disease | Pyridoxal phosphate / Phenylalanine / Adenosine phosphate / Tyrosine / Glutamic acid / ATP / Calcium / Magnesium cation / Iron / Acetoacetic acid / Oxogluric acid / Flavin adenine dinucleotide / Phenylpyruvic acid / Pyrophosphoric acid / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Tyrosinemia Type I |  | Disease | Pyridoxal phosphate / Ademetionine / Ascorbic acid / Aspartic acid / Tyrosine / Glutamic acid / NADH / Sapropterin / Norepinephrine / Epinephrine / Dopamine / Levodopa / Calcium / Magnesium cation / Iron / Zinc / 2-(3,4-Dihydroxyphenyl)Acetic Acid / Acetoacetic acid / Methylamine / 1,2-Dihydroxybenzene / Oxogluric acid / Flavin adenine dinucleotide / Pyrroloquinoline Quinone / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Tyrosinemia Type I |  | Disease | Pyridoxal phosphate / Ademetionine / Ascorbic acid / Aspartic acid / Tyrosine / Glutamic acid / NADH / Sapropterin / Norepinephrine / Epinephrine / Dopamine / Levodopa / Calcium / Magnesium cation / Iron / Zinc / 2-(3,4-Dihydroxyphenyl)Acetic Acid / Acetoacetic acid / Methylamine / 1,2-Dihydroxybenzene / Oxogluric acid / Flavin adenine dinucleotide / Pyrroloquinoline Quinone / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Tyrosinemia, Transient, of the Newborn |  | Disease | Pyridoxal phosphate / Ademetionine / Ascorbic acid / Aspartic acid / Tyrosine / Glutamic acid / NADH / Sapropterin / Norepinephrine / Epinephrine / Dopamine / Levodopa / Calcium / Magnesium cation / Iron / Zinc / 2-(3,4-Dihydroxyphenyl)Acetic Acid / Acetoacetic acid / Methylamine / 1,2-Dihydroxybenzene / Oxogluric acid / Flavin adenine dinucleotide / Pyrroloquinoline Quinone / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Tyrosinemia, Transient, of the Newborn |  | Disease | Pyridoxal phosphate / Ademetionine / Ascorbic acid / Aspartic acid / Tyrosine / Glutamic acid / NADH / Sapropterin / Norepinephrine / Epinephrine / Dopamine / Levodopa / Calcium / Magnesium cation / Iron / Zinc / 2-(3,4-Dihydroxyphenyl)Acetic Acid / Acetoacetic acid / Methylamine / 1,2-Dihydroxybenzene / Oxogluric acid / Flavin adenine dinucleotide / Pyrroloquinoline Quinone / Maleic acid / 4-Hydroxyphenylpyruvic acid / Homogentisic acid |
| Ubiquinol Drug Metabolism Pathway |  | Metabolic | Ubiquinol |
| Ubiquinone Biosynthesis |  | Metabolic | Ademetionine / Pyrophosphoric acid / 4-hydroxybenzoic acid |
| Ubrogepant Predicted Metabolism Pathway |  | Metabolic | Mesoheme / Ubrogepant |
| Udenafil Predicted Metabolism Pathway |  | Metabolic | Mesoheme / Udenafil |
| Ulobetasol Action Pathway |  | Drug Action | Glutathione / Ulobetasol / Dinoprostone / Calcium / Prostaglandin D2 / Mesoheme / Prostaglandin G2 / Arachidonic Acid |
| UMP Synthase Deficiency (Orotic Aciduria) |  | Disease | L-Glutamine / ATP / Calcium / Magnesium cation / Iron / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Thymidine monophosphate / Dihydrouracil / Dihydroorotic Acid / Orotic acid / Cytidine-5'-Triphosphate / Uridine / Orotidylic acid / Ribose-1-Phosphate / beta-Alanine / Flavin adenine dinucleotide / Flavin mononucleotide / Uracil / Uridine-5'-Diphosphate / Thymine / Uridine monophosphate / Deoxyuridine monophosphate / Pyrophosphoric acid / N-Carbamoylaspartic acid / Thymidine |
| UMP Synthase Deficiency (Orotic Aciduria) |  | Disease | L-Glutamine / ATP / Calcium / Magnesium cation / Iron / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Thymidine monophosphate / Dihydrouracil / Dihydroorotic Acid / Orotic acid / Cytidine-5'-Triphosphate / Uridine / Orotidylic acid / Ribose-1-Phosphate / beta-Alanine / Flavin adenine dinucleotide / Flavin mononucleotide / Uracil / Uridine-5'-Diphosphate / Thymine / Uridine monophosphate / Deoxyuridine monophosphate / Pyrophosphoric acid / N-Carbamoylaspartic acid / Thymidine |
| Undecoylium chloride iodine complex Drug Metabolism |  | Metabolic | Undecoylium chloride iodine complex |
| Upadacitinib Drug Metabolism |  | Metabolic | Upadacitinib |
| Urea C-13 Drug Metabolism |  | Metabolic | Urea C-13 |
| Urea C-14 Drug Metabolism |  | Metabolic | Urea C-14 |
| Urea Cycle |  | Metabolic | Pyridoxal phosphate / Pyruvic acid / Arginine / Aspartic acid / Ornithine / L-Glutamine / Adenosine phosphate / Glutamic acid / Citrulline / NADH / Alanine / ATP / Calcium / Oxogluric acid / Urea / Pyrophosphoric acid / Maleic acid |
| Ureidopropionase Deficiency |  | Disease | Pyridoxal phosphate / Histidine / Aspartic acid / Glutamic acid / NADH / Calcium / Zinc / Pantothenic acid / Dihydrouracil / Oxogluric acid / beta-Alanine / Flavin adenine dinucleotide / Flavin mononucleotide / Uracil |
| Urokinase Action Pathway |  | Drug Action | Urokinase / Phylloquinone / Calcium |
| Valacyclovir Action Pathway |  | Drug Action | Valine / Valaciclovir / Acyclovir / Magnesium cation |
| Valdecoxib Action Pathway |  | Drug Action | Glutamic acid / Glutathione / Valdecoxib / Dinoprostone / Calcium / Magnesium cation / Zinc / Prostaglandin D2 / Mesoheme / Prostaglandin G2 / Arachidonic Acid |
| Valdecoxib Action Pathway (New) |  | Drug Action | Glutathione / Valdecoxib / Dinoprostone / Calcium / Mesoheme / Prostaglandin G2 / Arachidonic Acid |
| Valdecoxib Predicted Metabolism Pathway |  | Metabolic | Valdecoxib / Mesoheme |
| Valganciclovir Action Pathway |  | Drug Action | Ganciclovir / Magnesium cation / Valganciclovir |
| Valine, Leucine, and Isoleucine Degradation |  | Metabolic | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Oxogluric acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |